【摘要】目的探讨儿童脉络丛乳头状癌的临床、影像学表现及诊疗经验。方法回顾性分析1例儿童脉络丛乳头状癌患者的临床资料,并结合相关文献进行复习。结果患儿男,因“突发抽搐3 d”,门诊拟“左侧脑室肿瘤”收治入院。入院后完善相关检查,择期行侧脑室三角区入路肿瘤切除术,肿瘤全切。术后病理诊断为脉络丛乳头状癌。文献复习结果显示儿童脉络丛乳头状癌为比较罕见的中枢神经系统肿瘤,诊断存在一定难度。结论临床表现、影像学特点及病理学特征是诊断该病的主要依据;手术为首选治疗手段,放疗有一定疗效。
Abstract: Objective To investigate the clinical, imaging findings and diagnosis and treatment experience of choroid plexus carcinoma(CPC) in children. Methods The clinical data of a child with CPC were analyzed retrospectively, and the relevant literature was reviewed. Results The patient, male, was admitted to the hospital for “left ventricular tumor” due to “sudden convulsion for 3 days”. After admission, the relevant examinations were improved, and the tumor was resected through the lateral ventricular triangle approach at a selected time. The postoperative pathological diagnosis was CPC. The results of literature review showed that papillary carcinoma of the choroid plexus in children was a relatively rare tumor of the central nervous system, and it was difficult to diagnose. Conclusions Clinical manifestations, imaging features and pathological features are the major basis for the diagnosis of this disease. Surgical operation is the first choice of treatment at present. Radiotherapy has certain curative effect.